An unusual presentation of Gomm-Button disease: a diagnostic enigma

Nagapadma Lakamsani; Sridevi K.; Ramamurthy D. V. S. B.; Senthil Kumar A. L.; Akshay Jain Salecha

doi:10.18203/issn.2455-4529.IntJResDermatol20220501

Authors

Nagapadma Lakamsani Department of Dermatology, Venereology and Leprosy, Katuri Medical College and Hospital, Guntur, Andhra Pradesh, India
Sridevi K. Department of Dermatology, Venereology and Leprosy, Katuri Medical College and Hospital, Guntur, Andhra Pradesh, India
Ramamurthy D. V. S. B. Department of Dermatology, Venereology and Leprosy, Katuri Medical College and Hospital, Guntur, Andhra Pradesh, India
Senthil Kumar A. L. Department of Dermatology, Venereology and Leprosy, Katuri Medical College and Hospital, Guntur, Andhra Pradesh, India
Akshay Jain Salecha Department of Dermatology, Venereology and Leprosy, Katuri Medical College and Hospital, Guntur, Andhra Pradesh, India

DOI:

https://doi.org/10.18203/issn.2455-4529.IntJResDermatol20220501

Keywords:

Sweet syndrome, Tender subcutaneous and erythematous plaques, Neutrophilic infiltrate in the upper dermis, Leukocytoclastic vasculitis

Abstract

Gomm-Button disease (Sweet syndrome) typically presents with abrupt onset of tender skin lesions accompanied by fever and neutrophilia. Histopathology shows the presence of dense neutrophilic infiltrates, oedema without vasculitis. One of the criteria for diagnosis of sweets syndrome is the absence of vasculitis. However, recent reports suggest that vasculitis should not exclude the diagnosis. We present a case of Sweet syndrome with an atypical clinical and histopathological presentation.

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