A rare case report of progressive symmetric erythrokeratoderma in five generations of an Indian family

Anil Kumar Gupta, Kanishk Utkarsh Kaushik, Sushantika ., Shivangi Sachan


Erythrokeratoderma is a rare group of disorders of autosomal dominant inheritance characterised by localised erythema and hyperkeratosis. Within a broad spectrum of phenotypes atleast two are delineated: a) Erythrokeratoderma variabilis and b) Progressive symmetric erythrokeratoderma. Here we are reporting a case of progressive symmetric erythrokeratoderma in an Indian family where five successive generations were involved.


Erythrokeratoderma, Five generations, Autosomal dominant, Progressive symmetric erythrokeratoderma

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