A rare case report of progressive symmetric erythrokeratoderma in five generations of an Indian family

Anil Kumar Gupta; Kanishk Utkarsh Kaushik; Sushantika .; Shivangi Sachan

doi:10.18203/issn.2455-4529.IntJResDermatol20183174

Authors

Anil Kumar Gupta Department of Dermatology, B R D Medical College, Gorakhpur Uttar Pradesh
Kanishk Utkarsh Kaushik Department of Dermatology, B R D Medical College, Gorakhpur Uttar Pradesh
Sushantika . Department of Dermatology, B R D Medical College, Gorakhpur Uttar Pradesh
Shivangi Sachan Department of Dermatology, B R D Medical College, Gorakhpur Uttar Pradesh

DOI:

https://doi.org/10.18203/issn.2455-4529.IntJResDermatol20183174

Keywords:

Erythrokeratoderma, Five generations, Autosomal dominant, Progressive symmetric erythrokeratoderma

Abstract

Erythrokeratoderma is a rare group of disorders of autosomal dominant inheritance characterised by localised erythema and hyperkeratosis. Within a broad spectrum of phenotypes atleast two are delineated: a) Erythrokeratoderma variabilis and b) Progressive symmetric erythrokeratoderma. Here we are reporting a case of progressive symmetric erythrokeratoderma in an Indian family where five successive generations were involved.

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Author Biography

Sushantika ., Department of Dermatology, B R D Medical College, Gorakhpur Uttar Pradesh

Junior Resident Second year, Department of Dermatology

References

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