Multifocal linear morphea - a rare presentation with rapid progression and deformities in a young adult: a case report

D. Devi; R. Rajesh; V. Mohankumar; K. Revathi

doi:10.18203/issn.2455-4529.IntJResDermatol20242363

Authors

D. Devi Department of Dermatology, Venereology, and Leprology, Government Erode Medical College and Hospital, Perundurai Sanatorium, Erode, Tamil Nadu, India
R. Rajesh Department of Dermatology, Venereology, and Leprology, Government Erode Medical College and Hospital, Perundurai Sanatorium, Erode, Tamil Nadu, India
V. Mohankumar Department of Dermatology, Venereology, and Leprology, Government Erode Medical College and Hospital, Perundurai Sanatorium, Erode, Tamil Nadu, India
K. Revathi Department of Dermatology, Venereology, and Leprology, Government Erode Medical College and Hospital, Perundurai Sanatorium, Erode, Tamil Nadu, India

DOI:

https://doi.org/10.18203/issn.2455-4529.IntJResDermatol20242363

Keywords:

Linear morphea, Multiple sites, Young adult, Deformities

Abstract

Morphea or localized scleroderma, is an uncommon skin disorder characterized by skin thickening and hardening. This case report describes a late 20s married woman working at a spinning mill, who presented with a unique and rare manifestation of morphea. Over two years, she developed a linear black color thickening of the skin on her right upper limb, left lower limb, and abdomen, accompanied by deformities and functional impairments. The patient reported a rapid progression of hyperpigmented lesions and weakness, prompting medical consultation. Cutaneous examination revealed distinctive hyperpigmented, atrophic plaques with xerotic changes and flexion deformities. A biopsy from the chest confirmed localized scleroderma. Basic investigations were within normal limits. The patient was managed with weekly pulse therapy involving corticosteroids, resulting in some relaxation of skin tightness. This case highlights the importance of recognizing and promptly treating rare multifocal morphea presentations to prevent severe deformities and enhance the patient's quality of life. Long-term follow-up is essential to monitor treatment outcomes and disease progression.

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