Clinical presentation of bullous systemic lupus erythematosus in a pediatric patient: a case report

Diana M. Ibarra Tostado; Alejandra Romero Parra; Marisol Padilla Ramirez; Sharira M.  Lopez Lopez; Diana L. Macias Cedeño; Cinthya P. Reyes Enriquez; Maria J. Zorrilla Marina; Jose M. Zepeda Torres

doi:10.18203/issn.2455-4529.IntJResDermatol20232547

Authors

Diana M. Ibarra Tostado Department of Laboral Health, Universidad Autónoma de Guadalajara, Jalisco, México
Alejandra Romero Parra Department of dermatology, Hospital Civil “Fray Antonio Alcalde”, Guadalajara, Jalisco, Mexico
Marisol Padilla Ramirez Department of dermatology, Hospital Civil “Fray Antonio Alcalde”, Guadalajara, Jalisco, Mexico
Sharira M. Lopez Lopez Department of dermatology, Hospital Civil “Fray Antonio Alcalde”, Guadalajara, Jalisco, Mexico
Diana L. Macias Cedeño Department of dermatology, Hospital Civil “Fray Antonio Alcalde”, Guadalajara, Jalisco, Mexico
Cinthya P. Reyes Enriquez Department of dermatology, Hospital Civil “Fray Antonio Alcalde”, Guadalajara, Jalisco, Mexico
Maria J. Zorrilla Marina Department of dermatology, Hospital Civil “Fray Antonio Alcalde”, Guadalajara, Jalisco, Mexico
Jose M. Zepeda Torres Department of Mentoring, Universidad Autónoma de Guadalajara, Jalisco, México

DOI:

https://doi.org/10.18203/issn.2455-4529.IntJResDermatol20232547

Keywords:

Dermatology, Dermatosis, Skin diseases

Abstract

Bullous systemic lupus erythematosus (BSLE) is a rare blistering eruption that can occur in patients with systemic lupus erythematosus. Although 59 to 85% of patients will have skin manifestations, less than 5% will develop the bullous disease, which is even rarer (1%) in the pediatric population. We present the case of a 16-year-old female patient in whom a diagnosis of BSLE was made through clinical presentation, histological study by biopsy, and direct immunofluorescence. Due to the low incidence of cases reported in pediatric patients, it is possible that the diagnosis may not be made immediately, which is why we emphasize the importance of obtaining an accurate diagnosis and providing timely treatment.

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