Small vessel vasculitis: a rare case report

Pradnya Asutkar; Sushil Pande

doi:10.18203/issn.2455-4529.IntJResDermatol20231832

Authors

Pradnya Asutkar Department of Dermatology Venerology and Leprology, NKP Salve Institute of Medical Sciences and Research Centre, Nagpur, Maharashtra, India
Sushil Pande Department of Dermatology Venerology and Leprology, NKP Salve Institute of Medical Sciences and Research Centre, Nagpur, Maharashtra, India

DOI:

https://doi.org/10.18203/issn.2455-4529.IntJResDermatol20231832

Keywords:

Vasculitis, Proximal myopathy, Wegener’s granulomatosis, Vessel

Abstract

Small-vessel vasculitis is a rare immunological disease that affects arterioles, capillaries and venules. A 1-year-6-month-old male of non-consanguineous marriage came to the OPD with his mother with a complaint of swelling over bilateral legs for 3 days and rash over his body for 1 day. The swelling was increasing and gradually ascending upward. Systemic examination revealed S1, S2 +, and no murmur in CVS. Soft, NT, liver, spleen not palpable. The patient was admitted and routine investigations were sent. The case reported above had clinical spectrum with skin involvement as palpable purpura, nervous system involvement as peripheral neuropathy and proximal myopathy and hematological involvement, gastrointestinal involvement as vague abdominal pain.

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