Subcutaneous panniculitis-like T cell lymphoma: a rare entity and its cryptic journey through pregnancy

Surender Singh; Siddhi B. Chikhalkar; Aditi A. Shende; Vidya D. Kharkar; Prateek Oswal

doi:10.18203/issn.2455-4529.IntJResDermatol20214215

Authors

Surender Singh Department of Dermatology, Seth G. S. Medical College and KEM Hospital, Mumbai, Maharashtra, India
Siddhi B. Chikhalkar Department of Dermatology, Seth G. S. Medical College and KEM Hospital, Mumbai, Maharashtra, India
Aditi A. Shende Department of Dermatology, Seth G. S. Medical College and KEM Hospital, Mumbai, Maharashtra, India
Vidya D. Kharkar Department of Dermatology, Seth G. S. Medical College and KEM Hospital, Mumbai, Maharashtra, India
Prateek Oswal Private practitioner, Abhyankar Hospital, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/issn.2455-4529.IntJResDermatol20214215

Keywords:

Subcutaneous panniculitis like T cell lymphoma, Pregnancy, Lupus like presentation

Abstract

Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare form of skin lymphoma that primarily is localized to the subcutaneous adipose tissue and accounts for less than 1% of all peripheral T-cell lymphomas. It presents with multiple subcutaneous nodules or plaques on extremities and has poor prognosis if accompanied by hemophagocytic syndrome. Differential diagnosis is panniculitis, lupus panniculitis and leprosy. We report such a rare case of a female with lupus erythematosus (LE) panniculitis like presentation with favourable outcome to oral steroids in pregnancy.

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