Erythrokeratoderma variabilis: a case report

Authors

  • Yogesh Devaraj Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India
  • Ranga Swaroop Mukunda Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India
  • Rashmi R. Mallya Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India
  • Taranpreet Kaur Kalra Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India
  • Shaila Shree Devendra Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India

DOI:

https://doi.org/10.18203/issn.2455-4529.IntJResDermatol20212558

Keywords:

EKV, Genodermatosis, Hyperkeratotic plaque, Migratory erythema

Abstract

Erythrokeratodermia variabilis (EKV) was first described by Mendes da Costa. It is a rare heterogeneous group of inherited cornification disorders characterized by two distinct types of skin lesions: fixed hyperkeratotic plaques and sharply marginated, pruritic, migratory erythematous lesions. We report a case of EKV in a 44-year-old male patient.

Author Biographies

Yogesh Devaraj, Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India

Department of Dermatology 

Associate professor

Ranga Swaroop Mukunda, Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India

Department of Dermatology

Head of Department

Rashmi R. Mallya, Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India

Department of Dermatology

Junior resident

Taranpreet Kaur Kalra, Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India

Department of Dermatology

Junior Resident

Shaila Shree Devendra, Department of Dermatology, Adichunchanagiri Institute of Medical Sciences, Mandya, Karnataka, India

Department of Dermatology

Junior Resident

References

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Common JEA, O'Toole EA, Leigh IM, Thomas A, Griffiths WAD, Venning V et al. Clinical and Genetic Heterogeneity of Erythrokeratoderma Variabilis. J Invest Dermatol. 2005;125(5):920-7.

Srinivas SM, Dhar S. Erythrokeratodermia variabilis and erythrokeratoderma en cocardes: Case series with review of literature. Indian J Paediatr Dermatol. 2016;17:202-5.

Tiwary AK, Dixit A. Erythrokeratoderma Variabilis in a 6-Year-Old Child: An Uncommon Genodermatosis with Typical Presentation. J Pigmentary Dis. 2017;4(1):e108.

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Published

2021-06-24

Issue

Section

Case Reports