DOI: http://dx.doi.org/10.18203/issn.2455-4529.IntJResDermatol20212558

Erythrokeratoderma variabilis: a case report

Yogesh Devaraj, Ranga Swaroop Mukunda, Rashmi R. Mallya, Taranpreet Kaur Kalra, Shaila Shree Devendra

Abstract


Erythrokeratodermia variabilis (EKV) was first described by Mendes da Costa. It is a rare heterogeneous group of inherited cornification disorders characterized by two distinct types of skin lesions: fixed hyperkeratotic plaques and sharply marginated, pruritic, migratory erythematous lesions. We report a case of EKV in a 44-year-old male patient.


Keywords


EKV, Genodermatosis, Hyperkeratotic plaque, Migratory erythema

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References


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